Myotonic dystrophy (DM) is an inherited disorder transmitted in an autosomal dominant
fashion and characterized by myotonia with dystrophic involvement of muscles and other
multisystemic manifestations. It is the most common muscular dystrophy in whites. DM1, the
most common type of DM, is associated with conduction defects, tachyarrhythmia,
cardiomyopathy, and other cardiac disorders such as valvular diseases. The conduction
defects in patients with DM1 are progressive; therefore, these patients should undergo …